分析肾小管性酸中毒患儿的治疗及远期预后。方法对17例患儿进行3～14a随访。结果死亡3例；自然痊愈1例；2例间断治疗者，现有轻微肾钙化、体格矮小、步履困难；11例仍在接受治疗，5例随访4～6a身高达正常水平，除轻度骨骼畸形外无其他发现，6例随访5～8a身高仍未正常，见不同程度骨骼畸形。结论本病早期诊断、正规治疗、终生服药可取得较好疗效。 Analysis of treatment and long-term prognosis of children with renal tubular acidosis. Methods 17 cases of children were followed up for 3 ~ 14a. Results of 3 cases of death; natural recovery in 1 case; 2 cases of intermittent treatment, the existing slight renal calcification, short stature, walking difficulties; 11 cases are still under treatment, 5 cases were followed up 4 ~ 6a up to normal levels, with the exception of mild bones There were no other findings outside of the deformity. Six of the patients were followed up for a period of 5 to 8 years and the height was not normal. See the different degrees of skeletal deformity. Conclusion Early diagnosis of this disease, formal treatment, lifelong medication can achieve better efficacy.