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<正>线粒体神经胃肠型脑肌病(Mitochondrial Neurogastroint-estinal Encephalopathy Disease,MNGIE)是一种特殊类型的线粒体肌病,又被称为"多发性神经病伴眼肌麻痹、白质脑病、假性肠梗阻(polyneuropathy ophthalmoplegia leukoencephalop-athy and intestinal pseudo-obstruction,POLIP)","眼部及胃肠