本病有多种命名,为一种罕见的有特殊家族的胃肠息肉病,多发生在小肠,并伴有明显粘膜、口唇及皮肤的多发性色素斑点;国内报道不多,我科于86年曾见一例,现报告如下:患者许××,女,21岁,因阵发性腹痛五天于1986年2月19日腹痛加剧急诊入院,住院号12786。患者自一岁起口唇,面部逐渐出现呈棕 The disease has a variety of names, a rare family with special gastrointestinal polyposis, occurs in the small intestine, accompanied by obvious mucosa, lips and skin multiple pigment spots; domestic reports are few, our department in 86 In one case, the report was as follows: Patient XXXX, female, 21 years old, admitted to hospital on August 19, 1986 due to paroxysmal abdominal pain for five days. The hospitalization number was 12,786. The patient began to have a lip since the first year and his face gradually appeared brown