论文部分内容阅读
目的探讨儿童短QT间期综合征(SQTS)与恶性心律失常的预后意义。方法随机测量18例儿童常规12导联心电图(ECG)QTFridercia(QTfc)和QTNomogram(QTnc)间期,根据R-R间期(R-R)和心率(HR)计算QT间期校正值(QTFridercia、QTNomogram)。QTFridercia、QTNomogram间期≤300 ms为短QT间期,观察短QTFridercia、QTNomo-gram间期与恶性心律失常的关系。用奎尼丁、氟卡尼和除颤器(Implanted cardioverter-defibrillator)治疗观察其预后。结果 QTFridercia≤300 ms发生心律失常为100%,QTNomogram≤300 ms发生心律失常为100%;奎尼丁、氟卡尼可使QT间期值平均延长20 ms,减少恶性心律失常发生,P<0.05。单用奎尼丁、氟卡尼治疗2年内心律失常发生率QT Fridercia44.44%,QTNomogram 44.44%;死亡率分别为11.11%、11.11%。除颤器治疗6例SQTS患者在2年的观察中无恶性心律失常发生和死亡率发生,P<0.05。结论短QT间期与恶性心律失常有关;奎尼丁、氟卡尼能延长QT间期,可减少恶性心律失常发生;ICD能有效防止恶性心律失常的发生率和死亡率。
Objective To investigate the prognostic significance of children with short QT syndrome (SQTS) and malignant arrhythmia. Methods QTFridercia (QTfc) and QTNomogram (QTnc) interval were measured in 18 children with conventional 12-lead electrocardiogram (ECG) and QT interval correction (QTNomogram) was calculated according to R-R interval and heart rate (HR) QTFridercia, QTNomogram interval ≤ 300 ms for the short QT interval to observe the relationship between short QTFridercia, QTNomo-gram interval and malignant arrhythmia. The prognosis was treated with quinidine, flecainide and defibrillator (defibrillated cardioverter-defibrillator). Results QTFridercia ≤ 300 ms arrhythmia was 100%, QTNomogram ≤ 300 ms arrhythmia was 100%; quinidine, flecainide QT interval can be an average of 20 ms, reducing the incidence of malignant arrhythmias, P <0.05 . The incidences of arrhythmia with QNF and QNF alone within two years after treatment with quinidine and flecainide alone were 44.44% and 44.11%, respectively; the mortality rates were 11.11% and 11.11%, respectively. Treatment of defibrillators Six patients with SQTS had no malignant arrhythmia and mortality at 2 years of observation, P <0.05. Conclusions Short QT interval is associated with malignant arrhythmia; quinidine and flecainide can prolong the QT interval and reduce the occurrence of malignant arrhythmia; ICD can effectively prevent the incidence of malignant arrhythmia and mortality.