高雪氏病是一种罕见病,现将我院外科治疗的1例报告如下: 患者王×,男,11岁,陕西省靖边县人。住院号130416。因左上腹无痛性包块6年入院。患者自幼发育及活动能力较同年龄儿童为差,瘦小、乏力、懒动、进食少。经常鼻衄、皮肤出血。自6岁时发现左上腹起一包块,增大迅速。无黑便及呕血。当地医院曾诊断“巨脾”“脾功能亢进”转来我院求治。无肝炎、黄疸病史,平时不感四肢及脊背疼痛。家族中父母健在,其三哥因左上腹包块 High snow disease is a rare disease, now a case of surgical treatment in our hospital as follows: Patient Wang ×, male, 11 years old, Jingbian County, Shaanxi Province. Hospital number 130416. Due to the left upper abdomen painless mass 6 years admitted. Patients with early childhood development and activity than children of the same age as poor, thin, fatigue, lazy move, eating less. Often nose, skin bleeding. From the age of 6 found that the upper left ventral mass, increased rapidly. No melena and hematemesis. The local hospital had diagnosed “spleen” “hypersplenism” to our hospital for treatment. No history of hepatitis, jaundice, usually do not feel limbs and back pain. Parents in the family alive, the third brother because of the left upper quadrant mass