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自身免疫性溶血性贫血(AIHA),是获得性溶血性贫血中的最常见者,可区分为温抗体型(WAIHA),冷凝集素综合征(CHD),以及阵发性冷性血红蛋白尿(PCH)三大类型。患者红细胞因受到自身抗体的作用,破坏加速而产生溶血,在骨髓造血不能代偿溶血的情况下,有可能会出现严重的贫血而需要输血治疗。作为现代输血治疗学和血液病学的难题之一,AIHA患者的输血治疗,必须注意以下问题。
Autoimmune hemolytic anemia (AIHA), the most common of acquired hemolytic anemias, can be distinguished as WAIHA, cold agglutinin syndrome (CHD), and paroxysmal cold hemoglobinuria PCH) three types. Patients with red blood cells due to the role of autoantibodies, destruction and acceleration of hemolysis, hemolysis in the bone marrow can not be compensated circumstances, there may be severe anemia and the need for blood transfusions. As one of the problems of modern blood transfusion therapy and hematology, the following problems must be paid attention to when transfusion treatment is performed in patients with AIHA.