目的 :提高对多房性囊性肾瘤的认识 ,熟悉对该病的诊断和治疗方法。方法 :回顾性分析 2例本病患者的临床资料并结合文献讨论本病的诊断和治疗。结果 :1例接受了患肾切除术 ,另 1例接受了肿瘤切除术。结论 :对儿童患者的治疗以患肾切除术为主 ,成人患者可行肾部分切除术或肿瘤切除术 Objective: To improve the knowledge of multilocular cystic nephroma, familiar with the diagnosis and treatment of the disease. Methods: The clinical data of 2 patients with this disease were retrospectively analyzed and the diagnosis and treatment of this disease were discussed in combination with the literature. Results: One patient underwent nephrectomy and the other patient underwent tumor resection. Conclusion: The treatment of children with nephrectomy is the main treatment for adult patients with partial nephrectomy or tumor resection