微囊性附属器癌(microcystic adnexal carcinoma,MAC)是一种少见的皮肤附属器肿瘤,1982年由Goldstein等~([1])首先报道。MAC多发生于头面部皮肤,尤其是口唇,而发生于舌部的MAC仅有1例报道。本文报道1例发生于舌部的MAC,活检时肿物由于缺乏独特的结构特点而误诊为基底细胞癌,在病灶扩大切除后注意到上皮下组织和神经周的肿瘤入侵,才明确了MAC的诊断。在此回顾诊断过程并结合文献复习,对该病的临床病理特征、病 Micocystic adnexal carcinoma (MAC) is a rare skin adnexal tumor that was first reported by Goldstein et al. ([1]) in 1982. MAC occurs in the head and face skin, especially the lips, while only one case of MAC occurred in the tongue. This article reports a case occurred in the tongue of the MAC, the biopsy tumor due to the lack of unique structural features misdiagnosed as basal cell carcinoma, enlarged lesions in the lesion after paying attention to the subepithelial tissue and nerve tumor invasion, only to clear the MAC diagnosis. In this review of the diagnosis and review of the literature, the clinical and pathological features of the disease, disease