先天性无牙颌畸形，为外胚叶发育异常疾病，临床上少见。1994年7月1日我科遇一例。白某．男性，12岁，因恒牙不萌出就诊。足月，顺产，第一胎，家族中无类似疾病，父母非近亲结婚，其母怀孕其间无特殊疾病及用药史。检查：一般情况良好，智力正常，眶距增宽，为4cm，小鼻孔，外 Congenital edentulous deformity, ectodermal dysplasia, clinically rare. July 1, 1994 in our case of a case. White one. Male, 12 years old, because of permanent teeth do not eruption treatment. Full-term, natural delivery, the first child, no similar disease in the family, parents marry non-relatives, their mothers during pregnancy there is no special disease and medication history. Check: the general condition is good, mental normal, widening of the orbital distance, 4cm, small nostrils, outside