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男,40岁。患者经常感两侧颞部胀痛,失眠、乏力、怕热、易汗,于1979年胸透时发现骨骼石化症,且经 X 片证实,掌骨片见骨质浓密,髓腔狭小;心电图示 PⅡ、Ⅲ、avF、V_3V_5V_6倒置,Pavr 直立;血色素8、5克:红细胞284万/mm3,网织细胞0.3%;硷性磷酸酶5.86金氏单位。讨论:本症首先由 Alber s~Schoenberg 氏描写,以终生骨质浓密、髓腔狭小(或几近消失)和贫血为特征,根据临床表现及全身各部位骨片所示,本例符合骨骼石化症的诊断。左房心律被认为
Male, 40 years old. Patients often feel both sides of the temporal pain, insomnia, fatigue, heat, sweat, chest pain in 1979 found that when the skeleton, and confirmed by X-ray, see the bone mass bone marrow, medullary narrow; electrocardiogram P Ⅱ, Ⅲ, avF, V_3V_5V_6 upside down, Pavr upright; hemoglobin 8,5 grams: 2.84 million erythrocytes / mm3, reticulocyte 0.3%; alkaline phosphatase 5.86 gold units. DISCUSSION: This disease was first described by Alber s ~ Schoenberg and characterized by a long lifetime of bone mass with narrow (or almost disappearing) marrow and anemia. According to clinical manifestations and bone fragments of various parts of the body, Diagnosis of disease. Left atrial rhythm is considered