肾上腺髓性脂肪瘤36例临床分析

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目的:探讨肾上腺髓性脂肪瘤的诊断及治疗。方法回顾性分析36例肾上腺髓性脂肪瘤患者的临床资料,总结诊断及治疗经验。36例患者术前均行常规生化检查、肾上腺皮髓质激素检测、CT检查,4例行腹部超声检查,1例行MRI检查。36例均手术治疗,其中33例行腹腔镜手术,3例行开放性手术。36例术后均行病理检查。结果36例手术均获成功,肿瘤直径10-130mm,术后病理32例为髓性脂肪瘤,4例为髓性脂肪瘤伴皮质腺瘤,且伴有皮质激素水平异常。术后随访2月-44月,肿瘤均未复发。结论肾上腺髓性脂肪瘤多无临床症状及内分泌功能,诊断主要依靠影像学检查,治疗方法根据患者临床症状、内分泌激素水平、肿瘤大小综合选择,有手术指证者首选腹腔镜手术,肿瘤直径≥8cm建议开放性手术治疗。肾上腺髓性脂肪瘤合并肾上腺皮质腺瘤罕见,应积极手术治疗。“,”Objective To explore the diagnosis and treatment of adrenal myelolipoma.MethodsClinical data of 36 cases of adrenal myelolipoma were analyzed retrospectively and summarize the experiences of diagnosis and treatment. Biochemical examination, adrenal cortex and medulla hormone test and CT examination were performed in all 36 patients, Ultrasonic examination was performed in 4 patients, MRI examination was performed in 1 patient. Surgery was performed in all 36 patients, open suigeries were conducted in 3 cases ang laparoscopic surgeries in 33 cases. Postoperative pathological examination were performed in all 36 patients.Results Tumors were all successfully removed. The size of tumors ranged from 10 to 130 mm in diameter. 32 cases were diagnosed pathologically as adrenal myelolipoma, 4 cases were adrenal myelolipoma accompanied withcortrical adenoma, and the adrenal cortex hormone in 4 cases were abnormal. 36 patients were followed up for 2 to 44 months with no recurrence.Conclusion There were no clinical symptoms and endocrine function inpatients with adrenal myelolipoma.
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