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慢性粒细胞性白血病(以下简称慢粒)急变的诊断,一般是以骨髓及/或末梢血中,原始细胞百分数的增加为主要依据。如原粒加早幼粒在骨髓及/或末梢血中超过20%,即可认为急变。但在少数慢粒患者,临床、骨髓及血象,都无急变表现,而在骨髓外局部区域发生急变。对这一现象,不同作者给予不同的名称,如:“髓外白血病”、“髓外原始细胞变”,“髓外原始细胞危象”“限局性原粒细胞瘤”等。我们遇到1
The diagnosis of acute myeloid leukemia (hereinafter referred to as CML) is mainly based on the increase of the percentage of primitive cells in bone marrow and / or peripheral blood. If the prills and promyelocytes in the bone marrow and / or peripheral blood more than 20%, can be considered rapid change. However, a small number of patients with chronic particles, clinical, bone marrow and blood, no rapid change in the performance, but in the extramedullary area of the sudden change. For this phenomenon, different authors give different names, such as: “extramedullary leukemia”, “extramedullary primitive cell change”, “Extramedullary primal cell crisis” “Bureau of the limited number of myeloblastoma” and so on. We met 1