湿疹、感染、血小板减少综合征是一免疫缺陷性疾病,又称Wiskott-Aldrich 综合征。我科分别于1986年7月及1987年8月收治2例,临床及实验室检查完全符合,现报道如下。例1,男,17月。因反复全身湿疹16个月,间隙性全身出血点13个月伴血尿2天而入院。患儿出生后半月全身出现湿疹,尤以面部、眉宇间、腹股沟为多,四个月皮肤出现散在出血点。查血小板50×10~9/L,外院诊断为血小板减少性紫癜,以后经常有鼻衄、牙龈出血、血小板持续在20～50×10~9/L。入院前一周有上呼吸道感染史。2天前明显肉眼血尿。患儿系 Eczema, infection, thrombocytopenia syndrome is an immunodeficiency disease, also known as Wiskott-Aldrich syndrome. Our department were in July 1986 and August 1987 were treated in 2 cases, clinical and laboratory tests fully consistent, are reported below. Example 1, male, 17 months. Due to repeated systemic eczema 16 months, intermittent systemic bleeding 13 months with hematuria 2 days and admitted to hospital. Children with eczema appeared after half a month, especially in the face, eyebrows, groin and more, four months the skin scattered bleeding. Check the platelet 50 × 10 ~ 9 / L, outside the hospital diagnosed as thrombocytopenic purpura, often after epistaxis, bleeding gums, platelets continued in the 20 ~ 50 × 10 ~ 9 / L. One week before admission, there is a history of upper respiratory tract infection. Obvious gross hematuria 2 days ago. Pediatric Department