本文报告一例肺母细胞瘤,并结合国内外文献收集的46例进行分析。本瘤多在肺末梢胸膜下(26/47例),72.3%呈球形或椭圆形。由上皮及间叶两个胚叶构成,状似胚胎肺。间叶性成分可形成梭形或圆形细胞肉瘤、软骨肉瘤及平滑肌肉瘤等。19例有各器官的转移,以肺、腹膜后多见。男多于女。87名在30～60岁之间。主要症状为咳嗽,咳血、胸痛、呼吸困难等。死亡率50%,生存5年以上达55%。 This article reports a case of pulmonary blastoma, and combined analysis of 46 domestic and international literature collections. The tumor was mostly subpleural in the lung (26/47 cases), and 72.3% was spherical or elliptical. It is composed of two epidermal and mesenchymal lobes, which resemble embryonic lungs. Invertebrate components can form spindle or round cell sarcoma, chondrosarcoma and leiomyosarcoma. In 19 cases, there were metastases of various organs, which were more common in the lung and retroperitoneum. More men than women. 87 are between 30 and 60 years old. The main symptoms are cough, hemoptysis, chest pain, and difficulty breathing. The mortality rate is 50%, and the survival rate is 55% over 5 years.