目的 :探讨 CT与 MRI对内耳畸形的诊断价值。方法 :通过 1例先天性内耳畸形病例的 CT与 MRI的影像学表现 ,并复习文献 ,分析内耳 CT与 MRI的成像特点及 MR膜迷路液成像优点。结果 :CT能清晰地显示内耳骨结构 ,而 MRI能清晰地显示膜迷路。结论 :CT与 MRI诊断内耳畸形优势互补 ,MR膜迷路液成像技术对内耳畸形有非常重要的诊断价值 Objective: To investigate the diagnostic value of CT and MRI in the deformity of the inner ear. Methods: The imaging features of CT and MRI in one case of congenital malformation of the inner ear were reviewed. The imaging characteristics of the CT and MRI in the inner ear were analyzed. Results: CT clearly showed the structure of the inner ear, while MRI clearly showed the labyrinthine membrane. Conclusion: CT and MRI are effective in diagnosing the deformities of the inner ear. MR imaging with MR imaging has a very important diagnostic value for deformities of the inner ear