原发性视网膜色素变性较为常见,但单侧者罕见,我科遇到一例。患者女性,38岁。因左眼视物不清就诊。患者于8年前偶然发觉左眼视物不清,晚上尤甚,虽经常服鱼肝油丸和中药,视力仍逐渐下降。无限外伤和其他眼病史,非近亲结婚,无小产史,家族中无同样眼病者。全身检查:未见异常,康瓦氏反应阴性。眼部检查:两眼外部检查无异常。视力: Primary retinitis pigmentosa is more common, but unilateral are rare, our department encountered a case. Patient female, 38 years old. Visually unclear due to left eye treatment. 8 years ago, patients occasionally found the left eye blurred vision, particularly at night, although often served cod liver oil pills and Chinese medicine, visual acuity is still gradually decreased. Infinite trauma and other history of eye disease, non-relatives marry, no history of small-scale, family members without the same eye disease. Whole body examination: no abnormalities, Kang Wah response negative. Eye examination: two external examination without exception. vision: