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目的:探讨骨斑点症的X线诊断价值,加深对骨斑点症的系统了解。材料与方法:对一个家族8例成员进行全身骨骼摄片调查,复习近几年国内文献报告的骨斑点症病因、病理和X线表现。结果:8例均有双侧对称的长骨干骺瑞大小不等、数量不一的圆形、椭固形、点状、结节状、索条状,甚至重叠、融合成大片状致密阴影,以膝、肘关节的两骨端为著,其余合骼极少受累。其中1例并发双侧股骨远端良性骨皮质缺损,另1例并发双侧髌骨发育异常。结论:X线检查是骨斑点症的主要诊断依据。临床上无症状,在偶然检查中发现,X线表现为全身多骨分布于松质骨的斑点状硬化就可确诊,如有家族遗传史和(或)并发其他体质性骨发育异常则更确定无疑。
Objective: To explore the diagnostic value of X-ray of bone spot syndrome and to deepen the systematic understanding of bone spot syndrome. Materials and Methods: 8 cases of a family member of the whole body bone imaging survey, reviewed in recent years, the domestic literature reported bone etiology, pathology and X-ray findings. Results: In all 8 cases, the long bones of bilateral symmetry had different sizes of epiphysis and varied numbers of round, oval solid, punctate, nodular, cord-like and even overlapping, blending into large flaky dense shadow, The knees, elbows of the two ends of the bone, the rest of the skeleton rarely involved. One case complicated with distal bilateral benign cortical bone defects, and the other cases complicated by bilateral patella development. Conclusion: X-ray examination is the main diagnosis of bone spot syndrome. Clinically asymptomatic, found in accidental examination, the X-ray showed that the whole body polygons scattered in the cancellous bone of the sclerosis can be diagnosed, if family history and / or complicated by other constitutional bone dysplasia is more certain undoubtedly.