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1.本文报告七例幼年Coats 病。临床表现有累及单眼、男性倾向、视力下降和瞳孔区有黄光反射。眼底镜检查可见视网膜脱离和视网膜下渗出。病理检查符合视网膜毛细血管扩张和微动脉瘤形成、渗出性视网膜全脱离。2.文献广泛讨论了以血管学说为主的发病机理,但迄今尚未最后确定病因因素。因此目前甚难有相应预防措施。作者等推测Coats 病象急性肾炎样、以全身过敏性感染性炎症为始动因素,主要累及视网膜血管病变。3.建议临床开展萤光血管造影检查,注意鉴别视网膜母细胞瘤和早期治疗。
This article reports seven cases of juvenile Coats disease. Clinical manifestations involving monocular, male predisposition, decreased vision and pupil area with yellow reflex. Fundus examination showed retinal detachment and subretinal exudation. Pathological examination consistent with retinal capillary dilatation and micro-aneurysm formation, exudative retinal detachment. 2. The literature extensively discusses the pathogenesis of vascular theory, but so far the cause has not yet been determined. So it is difficult to have the corresponding preventive measures. The authors speculate Coats disease like acute nephritis, systemic allergic infectious inflammation as a starting factor, mainly involving retinal vascular lesions. 3. It is recommended to carry out clinical fluorescent fluorescence angiography, pay attention to the differential diagnosis of retinoblastoma and early treatment.