先天性乳糜胸并不常见,但很易识别。而复发性先天性乳糜胸极其罕见。1967年Yancy 等复习了自发性乳糜胸31例,这些病例都是在出生后两个月内发现的,并且显示男患儿比女患儿高两倍。作者报告1例35岁女性,第一胎正常分娩女婴3400克。第二胎孕36周时患羊水过多症,超声证明胎儿水肿并伴双侧胸腔积液,经腹取胎血与胸腔穿刺,证实胸腔液体为乳糜液,胎血细胞分析为正常染色体核型,虽 Congenital chylothorax is uncommon but easily identifiable. Recurrent congenital chylothorax is extremely rare. In 1967 Yancy and other review of 31 cases of spontaneous chylothorax, these cases are found within two months after birth, and shows that men and women than children with children twice as high. The authors report a 35-year-old female with 3400 g of baby girl born on the first birth. The second gestational age 36 weeks when suffering from polyhydramnios, ultrasound proved that fetal edema and bilateral pleural effusion, fetus and thoracic abdomen through the abdominal puncture confirmed that the pleural fluid was chylous fluid, fetal hemocytes were analyzed for normal chromosome karyotype, although