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原发性降结肠浆细胞肉瘤极为罕见,国内尚无报告。Stephen于1972年在世界英文文献中收集到7例,Edward于1975年又报告1例,共8例。现将我院1例报告于下。患者男性,49岁,住院号10954,因左上腹持续性疼痛伴阵发性绞痛样加剧于1975年10月15日入院。1972年因大便变细曾做钡剂灌肠X线检查,无异常发现。1975年8月开始有大便次数增多,每天4~5次,伴里急后重,大便变细,食欲减退,体重下降。体检有左上腹压痛,未扪及肿块,肝脾不大,肠鸣音轻度亢进。全身浅表淋巴结未扪及,全身骨骼无压痛点。
Primary hypoplasia plasmacytosarcoma is extremely rare and has not been reported in China. Stephen collected 7 cases in the world’s English literature in 1972, and Edward reported 1 case in 1975, a total of 8 cases. Now report 1 case in our hospital. The patient, male, 49 years old, hospital number 10954, was hospitalized on October 15, 1975 because of persistent pain in the left upper quadrant with paroxysmal colic. In 1972, he had been barium enema X-ray examination because of thinning stools. No abnormalities were found. In August 1975, there was an increase in the frequency of bowel movements, 4 to 5 times a day, with tenesmus, thin stools, loss of appetite, and weight loss. Physical examination had left upper quadrant tenderness, non-convulsions and bumps, small liver and spleen, and mild bowel sounds. Whole body superficial lymph nodes were not palpable, and the whole body had no tender points.