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患儿女,2岁,因紫绀2年、咳嗽10余天、憋气伴阵发性紫绀加重1天入院。体检:T36.5℃,P160次/min,R30次/min。营养发育欠佳。全身皮肤及粘膜紫绀。球结膜充血,口唇及鼻周紫绀明显。胸廓略膨隆,双肺呼吸音粗,可闻及中小水泡音,心率160次/mi,心音低钝,肺动脉第二音亢进。腹软,肝脏肋下3~4cm。四肢末端紫绀,杵状指趾。彩超示心脏结构回声异常,室间隔缺如呈单心室,单心室形态呈左心室结构,共同房室瓣开
Children, 2 years old, 2 years because of cyanosis, cough for more than 10 days, suffocation with paroxysmal cyanosis increased 1 day admission. Physical examination: T36.5 ℃, P160 times / min, R30 times / min. Poor nutrition and development. Whole body skin and mucous membrane cyanosis. Conjunctival hyperemia, cyanosis of the lips and the nose obvious. Thorax slightly bulging, lung breath sounds crude, can be heard and small blisters sound, heart rate 160 times / mi, heart sound low blunt, pulmonary second tone hyperthyroidism. Abdomen soft, rib ribs 3 ~ 4cm. Extremities cyanosis, clubbed toe. Color ultrasound showed abnormal cardiac structure echo, absence of ventricular septal was single ventricle, single ventricular morphology was left ventricular structure, common atrioventricular valve open