This rare form of glaucoma is endemic for East Siberia region. This pathology is hereditary, it is transmitted through x-associat-ed recessive type by women-conductors to sick sons. Typical manifestation of this glaucoma is characteristic hypoplasia of iris stroma with its pigment layer uncovering. Pupil zone is always light gray, iris periphery is in the form of wide contrast ring of darker color. This two-colored hue is revealed in all patients and This rare form of glaucoma is endemic for East Siberia region. This pathology is hereditary, it is transmitted through x-associat-ed recessive type by women-conductors to sick sons. Typical manifestation of this glaucoma is characteristic hypoplasia of iris stroma with its pigment layer uncovering. Pupil zone is always light gray, iris periphery is in the form of wide contrast ring of darker color. This two-colored hue is revealed in all patients and