骨促结缔组织增生性纤维瘤(desmoplastic fibroma,DF)是一种罕见的骨肿瘤,由Jaffe[1]于1958年首先描述并命名。文献报道较少,儿童患者更为罕见。本文报道1例儿童DF,结合文献复习探讨其临床病理特点、诊断与鉴别诊断,以加强对该病的认识。1材料与方法1.1材料患儿男性,10岁。3年前发现步态有异常,1个月前X片检查发现右侧股骨近端肿块。查 Desmoplastic fibroma (DF) is a rare bone tumor that was first described and named by Jaffe [1] in 1958. Less literature reports, children are more rare. This article reports a case of children DF, combined with the literature review of its clinical and pathological features, diagnosis and differential diagnosis to enhance the understanding of the disease. 1 Materials and Methods 1.1 Materials Children, 10 years old. 3 years ago found abnormal gait, 1 month ago X-ray examination revealed the right proximal femur mass. check