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目的 探讨先天性主动脉弓离断（ＩＡＡ）的临床Ｘ线特点及Ｘ线平片诊断价值。材料和方法 回顾性分析７例（男３例，女４例，年龄３０天～１１岁，平均４岁）经心血管造影（ＡＣＧ）和（或）手术证实的ＩＡＡ患儿的临床、Ｘ线和ＡＣＧ表现及相互关系。结果７例全属Ａ１型，无Ｂ、Ｃ型，均合并心内畸形，术前Ｘ线平片符合诊断３例。主要的Ｘ线征象有：①气管居中（７例）；②主动脉结消失（７例）；③主动脉弓低位征（２例）；④升主动脉发育不良（４例）；⑤右上肺纵隔旁侧支循环血管影（６例）。结论Ｘ线平片诊断ＩＡＡ有局限性，但紧密结合临床可提示诊断，临床＋Ｘ线＋多普勒超声心动图（ＤＥ）的诊断模式可减少误（漏）诊率，确诊靠ＡＣＧ，对有造影禁忌证者，可采用ＭＲ来确诊。
Objective To investigate the clinical features of X-ray and the diagnostic value of congenital aortic arch disconnection (IAA). Materials and Methods Retrospective analysis of 7 cases (3 males, 4 females, aged 30 days to 11 years, average 4 years old) with clinical and X-ray findings of IAA confirmed by angiocardiography (ACG) and / or surgery And ACG performance and interrelationships. Results All of the seven cases were type A1, without type B and C, all with intracardiac deformity. The preoperative radiographs were consistent with the diagnosis of 3 cases. The main signs of X-ray were: ① tracheal center (7 cases); ② aortic node disappearance (7 cases); ③ aortic arch low sign (2 cases); ④ ascending aorta dysplasia (4 cases); Collateral vessels (6 cases). Conclusion X-ray diagnosis of IAA has limitations, but close clinical diagnosis can be prompted to diagnose, clinical + X-ray + Doppler echocardiography (DE) diagnosis mode can reduce the error rate, diagnosed by ACG, there are Contraindications for contrast may be confirmed by MR.