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儿童红细胞再生障碍的特点是红细胞生成障碍,而白细胞和血小板正常。此病不是获得的就是体质的(先天的或遗传的)。体质性疾病通常是持久的,而获得的疾病经常是暂时的,因此,要区别于成人纯红再生障碍。由于儿童贫血的治疗和予后取决于诊断,所以要对每种类型的特点加以叙述: 体质性红细胞再生障碍:Diamond-Blackfan贫血1936年首次叙述了非全血细胞减少的儿童贫血,1938年再次报告。到目前为止已报告200多例,并且作了文献复习,其诊断标准包括:1.婴儿早期发病,通常是正色素性、大细胞性贫血、网织细胞减少。2.骨髓细胞
Pediatric erythrocyte aplastic disorder is characterized by disorders of erythropoietin, while normal white blood cells and platelets. The disease is not acquired (physical or genetic). Constitutional diseases are usually persistent, and the acquired diseases are often transient and, therefore, different from adult pure redness disorders. Since the treatment and prognosis of childhood anemia depends on the diagnosis, each type of trait should be described: Constitutional Red Cell Aplasia: Diamond-Blackfan Anemia For the first time in 1936 the anemia of children with non-pancytopenia was recounted, and again in 1938 . So far has been reported more than 200 cases, and made a review of the literature, the diagnostic criteria include: 1. The early onset of infants, usually positive pigment, large cell anemia, reticulocyte reduction. 2. Bone marrow cells