MURCS综合征是Mayer-Rokitansky-Kuster-Hauser综合征(MRKH综合征)中的一个类别,临床主要表现为先天性子宫阴道发育不全,合并肾脏畸形、骨骼畸形、心脏畸形。MURCS综合征临床少见,常按典型或非典型MRKH综合征诊断和处理,易漏诊其他畸形。现结合文献复习报道如下。1临床资料患者,女性,18岁,因“第二性征发育4年无月经来 MURCS syndrome is a class of Mayer-Rokitansky-Kuster-Hauser syndrome (MRKH syndrome), the main clinical manifestations of congenital uterine vaginosis, with renal deformity, skeletal deformity, cardiac malformations. MURCS syndrome is clinically rare, often diagnosed and treated by typical or atypical MRKH syndrome, misdiagnosis of other deformities. Now combined with the literature review reported below. 1 clinical data patients, women, 18 years old, because of ”secondary sexual signs of development of 4 years without menstruation