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肥厚性心肌病(Hypertrophiccardiomyopathy,HCM)为常染色体显性遗传疾病,约有50%左右有家族聚集性,又称"家族聚集性心肌病(Familialhypertrophiccardiomyopathy,FHC)。根据肥厚的部位不同,Maron~([1])将HCM分为:(1)前室间隔肥厚;(2)前间隔、后间隔均肥厚;(3)室间隔与左室前侧壁均增厚,可累及后间壁和/或左室侧壁;(4)仅累及心尖部。按血流动力学分型分为梗阻型肥厚性心肌病与非梗阻型肥厚性心肌病。由于心室肌肥厚的部位及程
Hypertrophic cardiomyopathy (HCM) is an autosomal dominant genetic disease, with about 50% familial aggregation, also known as familial hypertrophic cardiomyopathy (FHC) .According to the hypertrophic site, Maron ~ (1) HCM is divided into: (1) anterior septal hypertrophy; (2) anterior septum and posterior septum are hypertrophy; (3) ventricular septal and left ventricular anterior thickened wall can affect the posterior wall and / Or left ventricular wall; (4) only involving the apical part.According to hemodynamic classification is divided into obstructive hypertrophic cardiomyopathy and non-obstructive hypertrophic cardiomyopathy .Because ventricular hypertrophy of the site and the process