膀胱畸形是新生儿期少见病。在Campbell氏19,000例小儿尸检中仅有7例为膀胱畸形,先天性巨大膀胱则更属少见,现将我院1987年1月遇到1例报道如下。男婴,2天,第一胎,孕40周,出生体重3500g,出腹困难。产后即发现患儿腹围大,口周紫绀,呼吸平稳。娩出时排胎便一次,小便一次。因腹围大,产科诊为腹腔脏器先天性畸形转入儿科。母妊娠前4个月,恶心呕吐严重,以致不能进食,无服药史,未接触过特殊化学物质和放射线,父母非近亲婚配。体检:体温36.3℃。脉搏112次。呼吸44次。反应好,呼吸平稳,鼻唇周围发绀。胸廓对称,两肺无罗音。心律齐,无杂音。腹向两侧扩大,腹壁静脉明显,肝脾未及。腹中部叩诊鼓音,两侧浊 Bladder malformations are rare in the neonatal period. In Campbell ’s 19,000 autopsy in children only 7 cases of bladder malformations, congenital giant bladder is even more rare, now in our hospital in January 1987 encountered a reported as follows. Baby boy, 2 days, the first child, 40 weeks pregnant, birth weight 3500g, abdominal difficulties. After childbirth found that children with abdominal circumference, perioral cyanosis, stable breathing. Childbirth row will be once, urinate once. Due to abdominal circumference, obstetric diagnosis of abdominal organ congenital malformations into pediatrics. In the first 4 months of pregnancy, nausea and vomiting were so severe that they could not eat, had no history of taking medication, had not been exposed to any special chemical substances and radiation, and had non-relatives and maternity. Physical examination: body temperature 36.3 ℃. Pulse 112 times. Breathing 44 times. Response is good, breathing steady, cyanosis around the nose and lip. Symmetrical thorax, lungs without rales. Qi heart, no noise. Belly to both sides of the expansion, abdominal veins obvious, liver and spleen not yet. Central percussion drum sound, both sides turbid