脊髓髓内肿瘤占中枢神经系统肿瘤不足10%,大多是室管膜瘤和星形细胞瘤。本文报告2例形态学和免疫组化表型比较特殊的脊髓髓内乳头状肿瘤。例1,7岁。胸段脊髓髓内肿瘤。外科切除后3年复发,先后在腰段脊髓、小脑、颞叶和颈静脉孔部位发现转移。初次手术病理诊断:乳头型室管膜瘤。颞叶肿瘤出现后再手术,组织学诊断与胸段脊髓髓内肿瘤相似。8 Spinal intramedullary tumors accounted for less than 10% of central nervous system tumors, mostly ependymoma and astrocytoma. This article reports 2 cases of morphological and immunohistochemical phenotype of spinal cord intramedullary papillary tumors. Example 1,7 years old. Thoracic spinal cord intramedullary tumors. 3 years after surgical resection recurrence, successively in the lumbar spinal cord, cerebellum, temporal lobe and jugular foramen found metastases. The first surgical pathological diagnosis: papillary ependymoma. Tumors in the temporal lobe were surgically treated and histologically similar to thoracic spinal intramedullary tumors. 8