先天性心脏病可合并冠状动脉的起源及分布异常,尤其多见于法鲁氏四联症、大血管转位、永存动脉干及单心室等。认识这些冠状动脉(简称冠脉)畸形,不仅可以作为鉴别诊断的重要线索,而且可提高外科治疗的成功率。由于心血管手术而损伤起源及(或)分布异常的冠状动脉而引起严重心肌缺血,甚至死亡 Congenital heart disease can be combined with the origin and distribution of coronary artery abnormalities, especially common in Farh’s tetralogy of Fallot, major vessel transposition, permanent arterial and single ventricle. Understanding these coronary arteries (referred to as coronary artery) deformity, not only can be used as an important clue to differential diagnosis, but also improve the success rate of surgical treatment. Due to cardiovascular surgery and damage the origin and (or) distribution of abnormal coronary arteries causing severe myocardial ischemia, and even death