伴有异常蛋白血症的血管免疫母细胞淋巴结病(AILD)是一种最近述及的具有充分临床病理特征的疾病。以前有人将类似这一临床病理改变的疾病称为弘慢性浆细胞肉瘤,慢性多能性免疫细胞增生综合征,淋巴肉芽肿 X 等疾病。最近用免疫母细胞淋巴结病来描述另一种可能是从 AILD 分化出来的疾病,但其与AILD 区别不大,本文将两者都视为 AILD。迄今报告的 AILD 已超过650例。本文试就本病下述各个方面进行评述。 Angio-immunoblastic lymphadenopathy (AILD) with anaphylactoidosis is a recently described disease with a full clinicopathological profile. Some people in the past will be similar to the clinical pathological changes of the disease known as Hong chronic plasma cell sarcoma, chronic multiple immune cell proliferation syndrome, lymphogranuloma X and other diseases. Recently, immunoblastic lymphadenopathy has been used to describe another disease that may have differentiated from AILD, but it is not much different from AILD and both are considered AILD in this article. AILD reported to date has been more than 650. This article tries to comment on the following aspects of this disease.