脱髓鞘性假瘤(demyelinating pseudotumor)是一种表现为占位效应的中枢神经系统脱髓鞘病变,临床较为少见,影像学检查常以局灶、孤立的肿块存在,故易被误诊为肿瘤。该病在1979年首先由Vander Velden报告,各年龄段均可发病,以青少年多见;无性别差异。大多位于大脑半球白质,偶尔累及小脑白质和脊髓。 Demyelinating pseudotumor (demyelinating pseudotumor) is a manifestation of the central nervous system demyelinating lesions, clinically rare, imaging often with focal, isolated mass exists, it is easily misdiagnosed as tumor . The disease was first reported by Vander Velden in 1979, with onset at all ages, more common among adolescents and no gender differences. Mostly located in the white matter of the cerebral hemispheres, occasionally involving the white matter and the spinal cord of the cerebellum.