遗传性外胚叶发育不全症(HereditaryectodermaL dysplasia ),又名遗传性无汗性外胚叶发育不全症(Hereditry anhidroticectodermaL dys-PLasia),是一种先天性发育畸形,十分罕见,国内外报道不多。我院曾诊治三例,报告于此。例1 男性,7岁,主团全口无牙,进食不便,于1980年6月12日将我科就诊。患儿系第一胎,足月顺产,体重仅2.5公斤,乳恒牙至今未萌,只能以稀软食维持生命,无头发,不出汗,夏天需用冷水洗澡,喜 Hereditary dermatode dysplasia (Hereditry anhidroticectodermaL dys-PLasia), is a congenital malformation of development, is very rare, not many reports at home and abroad . Our hospital had three cases of diagnosis and treatment, the report here. Example 1 Male, 7 years old, the main group full of no teeth, eating inconvenience, on June 12, 1980 to our department. Children with the first child, term full-term, weighing only 2.5 kg, the permanent teeth have not yet Moe, only to dilute soft food to maintain life, no hair, no sweating, summer need cold water bath, hi