先天性肺囊腺瘤样畸形(CCAM)是由于末端支气管呈瘤样过度生长,同时损害肺泡,在肺实质内形成有明显界限的一种病变,可在患儿出生后不久导致呼吸循环衰竭而死亡[1]。该症可分为3型。其中Ⅲ型预后不良,Ⅱ型并胎儿水肿及羊水增多,预后亦极差,一般均需外科干预,但往往在出生早期即失去手术机会[2]。从20世纪90年代起美国及欧洲一些国家已逐渐发展形成胎儿手术 Congenital cystic adenomatoid deformity (CCAM) is due to terminal bronchial tumor-like overgrowth, while damage to the alveoli, the formation of the lung parenchyma within a clear boundary of a disease, can be caused in children with respiratory failure shortly after birth and Death [1]. The disease can be divided into 3 types. Among them, type III has poor prognosis, type II with fetal edema and amniotic fluid increase, prognosis is also very poor, generally require surgical intervention, but often lose the chance of surgery in early life [2]. Since the 90s of 20th century, the United States and some European countries have gradually developed and formed fetal surgery