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最近几年,Q-T间期延长与心律失常的关系日益受到人们的重视。现将我院收治的7例Q-T间期延长并发尖端扭转型室速(TDP)报道如下: 临床资料一般情况:7例TDP患者中,女性6例,男性1例。年龄9-50岁(平均31.7岁)。3例为特发性Q-T延长综合症(LQTS);2例为心肌炎;1例冠心病、Ⅲ度A型房室传导阻滞;另外1例风心病、房颤、服用奎尼丁转律后。7例患者均有晕厥抽搐史,除1例发生一次晕厥外,其余6例多次发生晕厥。诱发因素:3例LQTS均在精神创伤和劳累后发病。1例房颤用奎尼丁转律过程中发生“奎尼丁晕厥”,尚有1例用乙胺碘呋酮
In recent years, the relationship between Q-T prolongation and arrhythmia has received more and more attention. Now in our hospital for treatment of 7 cases of Q-T prolongation of concurrent torsades de pointes (TDP) reported as follows: Clinical data General situation: 7 cases of TDP patients, 6 females, 1 males. Ages 9-50 (average 31.7 years). 3 cases of idiopathic QT prolongation syndrome (LQTS), 2 cases of myocarditis, 1 case of coronary heart disease, Ⅲ degree A-type atrioventricular block, and 1 case of rheumatic heart disease. After atrial fibrillation, . Seven patients had history of syncope convulsions, except one case of syncope occurred, the other six cases of syncope occurred repeatedly. Induced factors: 3 cases of LQTS are trauma and fatigue after the onset. One case of quinidine during atrial fibrillation occurred during the “Quinidine syncope”, there are 1 cases with amiodarone