颅内表皮样囊肿与皮样囊肿同属先天性上皮样肿瘤，本文对２５例的临床表现、辅助检查（包括头颅Ｘ线平片、ＣＴ和ＭＲＩ）、手术治疗及并发症的处理结合有关文献进行了复习。认为头颅ＣＴ及ＭＲＩ对本类疾病诊断帮助较大，手术切除并不十分困难，如能在显微镜下全切病灶并注意保护周围蛛网膜下腔，避免无菌性脑膜炎和交通性脑积水等并发症的发生，预后多较好。 Intracranial epidermoid cysts and dermoid cysts are both congenital epithelioid tumors, the 25 cases of clinical manifestations, laboratory examinations (including skull X-ray, CT and MRI), surgical treatment and complications associated with the treatment of the literature Review. It is considered that cranial CT and MRI are of great help in the diagnosis of this type of disease. Surgical resection is not very difficult. For example, the lesions can be totally cut under a microscope and the surrounding subarachnoid space can be protected to avoid aseptic meningitis and traffic hydrocephalus Complications, the prognosis is better.