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目的探讨脾窦岸细胞血管瘤(LCA)的临床病理特征、诊断与鉴别诊断要点。方法对3例脾窦岸细胞血管瘤进行常规病理检查、组织化学染色、免疫组化标记及电镜观察,并复习临床资料和相关文献。结果3例LCA患者均为中老年男性,组织学上肿瘤由大小不等的、互相吻合的血管性腔隙组成,腔隙被覆低柱状或立方形内皮细胞,无明显异型性。免疫表型:肿瘤细胞CD31、CD8、CD68、Ⅷ因子和lysozyme(+),CD34和D2-40(-)。结论LCA是很少见的、仅发生在脾的血管肿瘤,CT和B超检查可以发现病变,确诊还需依靠病理学及免疫组化检查。该肿瘤常伴有其他内脏疾病。
Objective To investigate the clinicopathological features, diagnosis and differential diagnosis of splenic sinusoid hemangiomas (LCA). Methods Three cases of hemangiomas of splenic sinusoid were routinely examined by histopathology, immunohistochemistry and electron microscopy. The clinical data and related literatures were reviewed. Results All 3 LCA patients were middle-aged and old men. Histologically, the tumors consisted of vascular cavities with different sizes and consistent with each other. The lacunae were covered with low columnar or cuboidal endothelial cells with no obvious atypia. Immunophenotype: Tumor cells CD31, CD8, CD68, Factor VIII and lysozyme (+), CD34 and D2-40 (-). Conclusions LCA is rare and only occurs in the splenic blood vessels. CT and B-ultrasound can detect lesions, and diagnosis depends on pathology and immunohistochemistry. The tumor is often accompanied by other visceral diseases.