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目的:探讨单骨骨纤维异常增殖症(fibrous dysplasia,FD)致长骨弯曲畸形的X线表现,提高对长骨FD的X线诊断水平。方法:通过对8例经手术病理证实,单骨FD致长骨弯曲畸形病例的X线征象的回顾,结合文献分析。所有病例均行常规正侧位X线检查。结果:病变位于胫骨5例,股骨1例,腓骨1例,桡骨1例:病变位于骨髓腔7例,骨皮质1例:病变范围均超过骨干长度的1/3且显示不同程度膨胀、弯曲畸形,最大成角为28度,最小为10度,无1例出现病理性骨折。主要X线表现:病变多数位于长管状骨骨髓腔,病变范围广,骨皮质膨胀、磨砂玻璃样、囊样、骨质硬化、骨干弯曲变形,病灶边界大多数清楚,且有不同程度硬化。结论:长骨FD弯曲畸形程度与病灶区内纤维组织含量有密切联系。
OBJECTIVE: To investigate the X-ray manifestations of long bone malformations caused by fibrous dysplasia (FD) and to improve the diagnostic value of long-bone FD in X-ray. Methods: A retrospective review of eight cases of pathologically confirmed, long-skeletal malformations of single-bone FD and combined with literature analysis. All cases underwent routine lateral radiographs. Results: The lesions were located in 5 cases of tibia, 1 case of femur, 1 case of fibula and 1 case of radial. The lesions were located in the medullary cavity in 7 cases and the cortical bone in 1 case. The lesions ranged from 1/3 of the backbone to inflated and flexed , The maximum angle of 28 degrees, the minimum is 10 degrees, no pathological fracture occurred in 1 case. The main X-ray findings: Most lesions located in the long tubular bone marrow cavity, a wide range of lesions, cortical expansion, frosted glass, cystic, bone sclerosis, bone bending deformation, the lesion border most clearly, and with varying degrees of hardening. CONCLUSION: The degree of FD bending and deformity of long bone is closely related to the content of fibrous tissue in the lesion area.