先天性肝内胆管囊状扩张（Caroli’s综合征）是青年人慢性胆汁郁积与肝石病的不常见原因，该病即使进行手术引流，其远期预后亦不良。本文报道用熊去氧胆酸（UDCA）治疗12例Caroll’s综合征与肝内结石的疗效。1981～1991年对20例Caroli’s综合征进行了评定，问例患肝内结石，其 Congenital intrahepatic bile duct dilatation (Caroli’s syndrome) is an uncommon cause of chronic cholestasis and hepatolithiasis in young people whose long-term prognosis is poor even with surgical drainage. This article reports the use of ursodeoxycholic acid (UDCA) treatment of 12 cases of Caroll’s syndrome and intrahepatic stone curative effect. 20 cases of Caroli’s syndrome were evaluated from 1981 to 1991, and asked for liver stones