OsLer-Rendu-Weber病亦名遗传性出血性毛细血管扩张症,临床较为少见,合并巨大肝更罕见。现将本院收治1例报告如下。陈××男性,11岁,宝山区人,住院号1151。肝大11年,反复鼻衄5年。近3年来面部小血管扩张。本次因发热3天,咳嗽1周,诊断支肺炎、肝大待查,于1991年3月24日入院。足月剖腹产,出生体重3.4Kg。无出生后窒息及持续黄疸史。婴幼儿期无喂养困难及 OsLer-Rendu-Weber disease also known as hereditary hemorrhagic telangiectasia, clinical less common, more common in the merger of the liver is rare. Now this hospital admitted to a report as follows. Chen × × male, 11 years old, Baoshan District, hospital number 1151. Liver 11 years, repeated epistaxis 5 years. Small facial blood vessels have dilated in the past 3 years. The fever for 3 days, cough for 1 week, diagnosis of bronchiectasis, liver for future inspection, in March 24, 1991 admission. Full-term caesarean section, birth weight 3.4Kg. No postpartum asphyxia and a history of persistent jaundice. Infancy and no feeding difficulties