黑色素斑——胃肠道多发性息肉综合征,又称 Peutz—Jegher’s 综合征,是一种常染色体显性连锁遗传的疾病。在儿童中较为少见,我们发现一家姐妹二例,兹报告如下。病历摘要例1 女,8岁,住院号13976。1987年4月9日入院。2岁时发现口唇有黑色素斑点沉着,小如针尖,以后逐渐在齿龈部, Melanoma - Gastrointestinal polyposis syndrome, also known as Peutz-Jegher’s syndrome, is an autosomal dominant inherited disorder. Less common among children, we found two sisters, one of whom is as follows. Case history summary 1 female, 8 years old, hospital number 13976. April 9, 1987 admission. 2 years old found that the lips have melanin spots calm, as small as the tip, then gradually in the gums,