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本文报告32例腓骨肌萎缩症(PMA)患者的临床及肌电图(EMG)和神经传导速度(NCV)的改变。其中20例PMA患者的感觉神经传导速度(SNCV)减慢,正中神经SNCV:拇指到腕平均为21.0m/s,中指到腕平均22.7m/s、末端潜伏期(ML)平均为7.3ms;胫后神经SNCV:(足母)趾到踝平均为22.2m/s,ML平均为8.1ms,符合PMA Ⅰ型。另外12例患者的SNCV正常或轻度减慢,正中神经SNCV:拇指到腕平均为41.0m/s,中指到腕平均为47.0m/s,ML平均为3.2ms,胫后神经SNCV:(足母)趾到踝平均32.5m/s,ML平均为4.8ms,符合PMA Ⅱ型。二型NCV改变差异非常显著(P<0.01)。6例腓肠神经活检,5例符合NCV分型.提示详细的NCV检查是诊断本病重要而易行的手段。
This article reports the clinical and electromyogram (EMG) and nerve conduction velocity (NCV) changes in 32 patients with Charcot-Marie-Tooth Syndrome (PMA). The sensory nerve conduction velocity (SNCV) of 20 patients with PMA was slowed down. The median SNCV of the median nerve was 21.0m / s from the thumb to the wrist, 22.7m / s from the middle finger to the wrist, and the mean terminal latency (ML) was 7.3ms. The posterior nerve SNCV: (foot mother) ankle to the average of 22.2m / s, ML average of 8.1ms, consistent with PMA type Ⅰ. SNCV of the other 12 patients were normal or slightly slowed down. SNCV of median nerve was 41.0m / s from the thumb to the wrist, mean of the middle finger to wrist was 47.0m / s, ML was 3.2ms on average, SNCV of the posterior tibial nerve: Mother) ankle to the average 32.5m / s, ML average of 4.8ms, in line with PMA Ⅱ type. Type 2 NCV changes were significant differences (P <0.01). Six cases of sural nerve biopsy, 5 cases of NCV classification, suggesting that detailed NCV examination is an important and easy diagnosis of the disease means.