皮肌炎首在1863年由Wagner称为多发性肌炎,其后在1891年由Unverricht命名为皮肌炎。本病如病名所示,主要病变部位在皮肤和肌肉。但它是除了皮肤肌肉以外,也可并发各种内脏损害的全身性疾病。本病过去认为很少见,故未予重视。自从Klemperer提倡胶原病学说以来,始引人注目。本病的报告也日见增多。对本病的病因、病理、临床、治疗等方面作了种种探讨,发表了很多新的见解,在提出胶原病学说的疾患中,除本病外,尚有系统性红斑狼疮(SLE)、泛发性硬皮病(进行性全身性硬化症)等。这三种病的典型 Dermatomyositis was first described by Wagner in 1863 as polymyositis and later by Derveromycin in 1891 by Unverricht. The disease as the name shows, the main lesion in the skin and muscle. But it is in addition to the skin muscles, but also can be complicated by a variety of visceral damage systemic disease. The disease in the past that is rare, it is not taken seriously. Since Klemperer advocated the theory of collagen disease has begun to attract attention. The report of the disease is also increasing. On the etiology, pathology, clinical, treatment and other aspects of the made a variety of discussions, published a lot of new insights in the proposed collagen disease theory disorders, in addition to the disease, there are systemic lupus erythematosus (SLE), pan Scleroderma (progressive systemic sclerosis) and the like. Typical of these three diseases