目的　探讨肺母细胞瘤患者的临床特点及诊断、治疗方法。方法　回顾性分析8例肺母细胞瘤患者的临床资料,并结合文献对其临床表现和诊断、治疗方法进行分析。结果　肺母细胞瘤是一种罕见的恶性肿瘤,手术前很难确诊。主要症状为咳嗽、痰中带血、胸痛和发热。X线胸片示以周围型居多,病灶长径3~10cm,边缘清楚,还可见肺门及纵隔淋巴结肿大。支气管镜检查可见肿物阻塞管腔或支气管狭窄, 1例活检可见腺棘细胞癌。8例均行手术治疗并经病理确诊;术后随访,仅1例生存2年以上。结论　肺母细胞瘤患者预后差,外科手术是主要的治疗方法。 Objective To investigate the clinical features, diagnosis and treatment of patients with pulmonary blastoma. Methods The clinical data of 8 patients with pulmonary blastoma were analyzed retrospectively. The clinical manifestations, diagnosis and treatment were analyzed based on the literature. Results Pulmonary blastoma is a rare malignancy that is difficult to diagnose before surgery. The main symptoms are cough, bloody sputum, chest pain and fever. X-ray showed the majority of peripheral type, the lesion diameter of 3 ~ 10cm, clear edge, but also visible hilar and mediastinal lymph nodes. Bronchoscopy showed tumor obstruction lumen or bronchial stenosis, biopsy can be seen in 1 case of pancreatic adenocarcinoma. Eight patients underwent surgical treatment and pathological diagnosis; after follow-up, only 1 case survived more than 2 years. Conclusion The prognosis of patients with pulmonary blastoma is poor, and surgery is the main treatment.