患者女 ,18岁。聋哑 17年 ,双眼视力进行性下降伴夜盲 5年 ,加重 1周 ,于 2 0 0 0年 8月 2 5日就诊。全身检查未见异常。眼部检查 :视力右眼 0 .5 ,针孔 0 .5 ;左眼 0 .0 8,针孔 0 .1,双眼视力不能矫正。眼压 :右眼 2 6 mm Hg(1mm Hg=0 .133k Pa) ,左眼2 5 mm Hg。双眼外眼正常 Patient female, 18 years old. 17 years of deaf and mute, progressive decline in binocular vision with night blindness for 5 years, an increase of 1 week, on August 20, 2000 treatment. No abnormalities in the whole body examination. Eye examination: Right eye 0 .5, pinhole 0 .5; left eye 0. 0 8, pinhole 0 .1, binocular vision can not be corrected. Intraocular pressure: 26 mm Hg for the right eye (1 mm Hg = 0.133 k Pa) and 25 mm Hg for the left eye. Outer eyes normal