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我院曾收治胃肠型恶性组织细胞病(恶组病)2例报告如下。例1,男,27岁。因高热10天,进行性肝脾肿大和全血细胞减少入院。1个多月前曾因急性阑尾炎在外院2次手术,此后一直不规则发热伴脾肿大和白细胞减少,骨髓检查和淋巴结活检均阴性。入院时检查发现:高热39℃;肝肋力3cm;脾达脐平。红细胞3.5×10~(12)/L,血红蛋白81g/L,白细胞1.3×10~9/L,血小板20×10~9/L;髂骨穿刺,髓象再生低下;胸骨穿
Our hospital has received gastrointestinal malignant histiocytosis (croup disease) 2 cases are as follows. Example 1, male, 27 years old. Due to fever for 10 days, progressive hepatosplenomegaly and pancytopenia hospitalization. More than one month ago, acute appendicitis was performed in the second hospital for two surgeries. Irregular fever followed by splenomegaly and leukopenia, bone marrow examination and lymph node biopsy were all negative. Examination found at admission: high fever 39 ℃; liver ribs force 3cm; spleen up umbilical flat. 3.5 × 10 ~ (12) / L of red blood cells, 81g / L of hemoglobin, 1.3 × 10 ~ 9 / L of white blood cells and 20 × 10 ~ 9 / L of platelets;