婴幼儿良性癫痫是一组婴幼儿发病的癫痫,1989年癫痫与癫痫综合征的国际分类中,仅列出了一个婴儿期起病的特发性癫痫综合征,即婴儿良性肌阵挛性癫痫。近年来国内外文献相继报道了一些新的婴幼儿良性癫痫综合征,现将有关文献进行综述。1 良性家族性新生儿惊厥本病为常染色体显性遗传,1964年首先报道,临床较少见。临床特点是足月儿出生后2～4天出现惊厥,开始呈强直姿势,眼斜视,继而肢体阵挛性抽动或呼吸暂 Infants and young children with benign epilepsy is a group of infantile onset of epilepsy, epilepsy and epilepsy syndrome in 1989, the international classification, only listed one infancy onset of idiopathic epilepsy syndrome, that is, infant benign myoclonic epilepsy . In recent years, domestic and foreign literatures have reported some new infants and children with benign epilepsy syndrome, the relevant literature is now reviewed. 1 benign familial neonatal convulsion This disease is autosomal dominant, first reported in 1964, the clinical less common. Clinical features of full-term children 2 to 4 days after birth, convulsions, began to be straight posture, ocular strabismus, and then limbs clonic tics or breathing temporarily