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目的分析肺泡蛋白沉着症的CT表?特点,以提高诊断及鉴别诊断水平。方法回顾性分析5例经病理证实的肺泡蛋白沉着症的CT表现。结果 CT表现为双肺弥漫分布的片状磨玻璃样气腔实变影;小叶内及小叶间间隔增厚,形成“铺路石征”样表现;病变与正常组织分界清晰,形成“地图样”分布。结论特征性影像表现结合临床可提出本病诊断。
Objective To analyze the CT features of pulmonary alveolar proteinosis in order to improve the diagnostic and differential diagnosis. Methods A retrospective analysis of 5 cases of pathologically confirmed pulmonary alveolar proteinosis CT findings. Results The CT manifestations were diffuse distribution of glass-like air-cavity realism in the double lung. The interlobular septa and interlobular septa were thickened to form a “paving stone sign”. The boundary between the diseased and normal tissues was clear and the “ Map pattern ”distribution. Conclusion The characteristic imaging findings combined with clinical diagnosis of the disease can be made.