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多发性神经纤维瘤并桥小脑角多发性蛛网膜囊肿临床少见,现将我院经手术及病理证实的一例报告如下。患者女,51岁。因左面颊阵发性刀割样剧痛,伴左耳鸣9年,于1985年12月16日入院。检查:神志清,颈后部有2个花生米大小皮下结节(病理检查为“神经纤维瘤”),左三叉神经Ⅱ、Ⅲ支分布区感觉减退,左耳听力减退,左口角有“触发点”。实验室硷查:出凝血时间正常。颅底及内耳孔 X 片未见明显异常。诊断:①多发性神经纤维瘤;②左三叉神经痛。12
Multiple neurofibromas and cerebellopontine angle Multiple arachnoid cysts are rare clinical cases now confirmed by surgery and pathology in our hospital are as follows. Female patient, 51 years old. Due to the left cheek paroxysmal knife-like pain, with left tinnitus 9 years, on December 16, 1985 admission. Examination: Consciousness, the back of the neck with 2 peanuts size subcutaneous nodules (pathological examination for the “neurofibroma”), left trigeminal nerve distribution of Ⅱ, Ⅲ feeling decreased, left ear hearing loss, left corner of the “trigger point”. Laboratory check: a normal clotting time. Skull and inner ear hole X-ray showed no significant abnormalities. Diagnosis: ① multiple neurofibromatosis; ② left trigeminal neuralgia. 12