Dand—Walker综合征是以后颅凹巨大囊肿,小脑发育不良为基础的小儿少见疾病,国内少见报道,现报告我们手术治疗的2例。 例1 女,12岁,头痛2年,走路不稳6个月就诊,平时头痛,无恶心、呕吐,曾服去痛片效果差。检查:发育营养一般,两眼可见水平眼震,眼底无水肿,步基宽,步态蹒跚,指鼻试验(+),跟膝胫试验(+),闭目难立征(+)。CT平扫:后颅凹中线部位可见巨大囊肿影,密度均匀,CT值8.6Hu,囊肿前界达脑干后缘,脑积水,增强扫描无强化改变,术中见囊肿同第四脑室 Dand-Walker syndrome is a giant cyst after skull concave, cerebellar dysplasia based on rare diseases in children, rarely reported in China, we report 2 cases of surgical treatment. Example 1 female, 12 years old, headache for 2 years, unsteady walking 6 months treatment, usually headache, no nausea, vomiting, had to take to the painkillers poor results. Check: the development of nutrition in general, both eyes can see the level of nystagmus, fundus without edema, gait width, gait hobbled, finger nasal test (+), with the knee shin test (+), closed eyes refractory extremity (+). CT scan: the posterior fossa midline part of a huge cyst visible shadow, uniform density, CT value 8.6Hu, the front of the cyst in the trailing edge of the brainstem, hydrocephalus, enhanced scan without enhancement, intraoperative see cyst with the fourth ventricle